The Annals of Thoracic Surgery, Vol 41, 664-666, Copyright © 1986 by The Society of Thoracic Surgeons
Attenuated pulmonary vascular obstructive disease in double-outlet right ventricle and mitral stenosis
GR Westerman, AF Tryka, JB Norton and SH Van Devanter
A young woman with double-outlet right ventricle, mitral stenosis, and high
systemic pulmonary artery pressure is described. Pulmonary vascular
morphometric analysis indicated considerably less pulmonary vascular
obstructive disease than might otherwise have been expected. Total repair
was performed and resulted in a marked fall in pulmonary artery pressure.
Pulmonary vascular morphometry may be indicated in selected patients before
palliative management is selected over complete repair.