The Annals of Thoracic Surgery, Vol 31, 70-77, Copyright © 1981 by The Society of Thoracic Surgeons
Repair of combined total anomalous pulmonary venous connection and anomalous systemic connection in early infancy
K Turley, H Tarnoff, R Snider and PA Ebert
A simple intraatrial reconstruction can be utilized in infants to
simultaneously correct both the systemic and pulmonary venous returns. Two
infants with polysplenia syndrome treated in the first months of life are
presented. One had levocardia and combined total anomalous pulmonary venous
connection (type II-Cardiac) and anomalous systemic venous connection. The
other had dextrocardia L-loop, L-normal great arteries, and combined total
anomalous pulmonary venous connection (type II-Cardiac) and anomalous
systemic venous connection. The posterior position of the systemic
atrioventricular valve and systemic ventricle in both patients allowed the
use of this reconstructive technique. The extensive size and transverse
position of this patch when used in the infant may require both continued
postoperative controlled ventilation until it stiffens and prolonged
attention to postoperative cardiac care until adaptation of the infant
heart to the new atria can occur. Early restudy and reoperation should be
performed if signs of stenosis develop.